Cystic Fibrosis Transmembrane Conductance Regulator
"Cystic Fibrosis Transmembrane Conductance Regulator" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A chloride channel that regulates secretion in many exocrine tissues. Abnormalities in the CFTR gene have been shown to cause cystic fibrosis. (Hum Genet 1994;93(4):364-8)
MeSH Number(s)
D12.776.157.530.400.175.125
D12.776.543.550.425.175.125
D12.776.543.585.400.175.125
Below are MeSH descriptors whose meaning is more general than "Cystic Fibrosis Transmembrane Conductance Regulator".
Below are MeSH descriptors whose meaning is more specific than "Cystic Fibrosis Transmembrane Conductance Regulator".
This graph shows the total number of publications written about "Cystic Fibrosis Transmembrane Conductance Regulator" by people in Harvard Catalyst Profiles by year, and whether "Cystic Fibrosis Transmembrane Conductance Regulator" was a major or minor topic of these publication.
To see the data from this visualization as text,
click here.
Year | Major Topic | Minor Topic | Total |
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1994 | 0 | 5 | 5 |
1995 | 1 | 2 | 3 |
1996 | 5 | 0 | 5 |
1997 | 5 | 2 | 7 |
1998 | 6 | 1 | 7 |
1999 | 6 | 0 | 6 |
2000 | 5 | 4 | 9 |
2001 | 7 | 3 | 10 |
2002 | 7 | 2 | 9 |
2003 | 4 | 4 | 8 |
2004 | 9 | 5 | 14 |
2005 | 5 | 5 | 10 |
2006 | 4 | 1 | 5 |
2007 | 7 | 3 | 10 |
2008 | 4 | 3 | 7 |
2009 | 10 | 7 | 17 |
2010 | 6 | 7 | 13 |
2011 | 8 | 1 | 9 |
2012 | 5 | 5 | 10 |
2013 | 4 | 2 | 6 |
2014 | 6 | 2 | 8 |
2015 | 8 | 6 | 14 |
2016 | 11 | 5 | 16 |
2017 | 13 | 5 | 18 |
2018 | 6 | 1 | 7 |
2019 | 8 | 7 | 15 |
2020 | 7 | 3 | 10 |
2021 | 7 | 10 | 17 |
2022 | 3 | 13 | 16 |
2023 | 2 | 16 | 18 |
2024 | 1 | 1 | 2 |
Below are the most recent publications written about "Cystic Fibrosis Transmembrane Conductance Regulator" by people in Profiles.
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Cystic Fibrosis Mice Are Highly Susceptible to Repeated Acute Pseudomonas aeruginosa Pneumonia after Intranasal Inoculation. Biomed Res Int. 2024; 2024:4769779.
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Elexacaftor/Tezacaftor/Ivacaftor Treatment and Depression-related Events. Am J Respir Crit Care Med. 2024 Feb 01; 209(3):299-306.
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Inflammatory Activity of Epithelial Stem Cell Variants from Cystic Fibrosis Lungs Is Not Resolved by CFTR Modulators. Am J Respir Crit Care Med. 2023 11 01; 208(9):930-943.
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Changes in fecal elastase-1 following initiation of CFTR modulator therapy in pediatric patients with cystic fibrosis. J Cyst Fibros. 2023 Nov; 22(6):996-1001.
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Transgenic ferret models define pulmonary ionocyte diversity and function. Nature. 2023 Sep; 621(7980):857-867.
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Red ginseng aqueous extract improves mucociliary transport dysfunction and histopathology in CF rat airways. J Cyst Fibros. 2023 Nov; 22(6):1113-1119.
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Cystic Fibrosis: "Ionocyte Modulators"? Am J Respir Cell Mol Biol. 2023 09; 69(3):250-252.
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CFTR Modulators for the Gastroenterologist. J Pediatr Gastroenterol Nutr. 2023 10 01; 77(4):445-447.
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Hidden CFSPID in CF patient registries? The Italian CF Registry experience. J Cyst Fibros. 2023 Nov; 22(6):1128-1129.
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Positive and negative impacts of elexacaftor/tezacaftor/ivacaftor: Healthcare providers' observations across US centers. Pediatr Pulmonol. 2023 09; 58(9):2469-2477.