Disease-associated mutant alpha-actinin-4 reveals a mechanism for regulating its F-actin-binding affinity.
Weins A, Schlondorff JS, Nakamura F, Denker BM, Hartwig JH, Stossel TP, Pollak MR. Disease-associated mutant alpha-actinin-4 reveals a mechanism for regulating its F-actin-binding affinity. Proc Natl Acad Sci U S A. 2007 Oct 09; 104(41):16080-5.
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Actinin
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Actins
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Amino Acid Substitution
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Animals
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Binding Sites
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Cells, Cultured
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Glomerulosclerosis, Focal Segmental
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Humans
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Kinetics
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Mice
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Mice, Knockout
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Mice, Mutant Strains
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Microfilament Proteins
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Microscopy, Electron, Transmission
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Models, Biological
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Models, Molecular
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Mutagenesis, Site-Directed
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Mutation
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Protein Binding
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Protein Structure, Tertiary
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Recombinant Fusion Proteins